Background. - Leiomyosarcomas of the digestive tract are very rare in
children. They must be differentiated from benign tumors (leiomyoma, s
chwannoma...) and from other malignant tumors, sometimes with the aid
of immuno-histochemical study. Case report. - A five-year old girl suf
fered from an abdominal mass associated with fever and alteration of t
he general condition. An ileal turner, 8 cm in diameter was resected.
Histological and immunohistochemical studies (anti-vimentin antibodies
, anti-actin antibodies and PS100) confirmed the diagnosis of leiomyos
arcoma. Uncomplete adjuvant chemotherapy failed to prevent relapse of
the turner. Conclusion. - This case confirms the bad prognosis of such
a tumor.