SUCCESSFUL STAGED SURGICAL-CORRECTION OF CONGENITAL SEGMENTAL SPINAL DYSGENESIS AND COMPLETE ROTARY SUBLUXATION OF THE THORACOLUMBAR SPINE IN AN INFANT

Congenital segmental spinal dysgenesis is a rare lesion that usually i s associated with neurological deficits. Affected infants who are neur ologically intact may suffer progressive kyphosis and subsequent neuro logical deterioration. Results of external casting, laminectomy with s pinal fixation, or bone grafting of the defect have been disappointing . The authors present a successful staged surgical management scheme c onsisting of complete resection of the dysraphic vertebral bodies, mai ntenance of normal vertebral distance with rib strut grafting, and fus ion with autogenous bone. Copyright (C) 1996 by W.B. Saunders Company