This report describes a case of a rare, dorsally placed enterogenous c
yst at the craniocervical junction. The patient had preoperative magne
tic resonance imaging studies, followed by microsurgical removal of th
e cyst. The patient made an uneventful recovery from the surgery. Path
ological examination revealed an enterogenous cyst. Alb though enterog
enous cysts are more commonly found in the lower cervical or thoracic
spine, it is important to recognize that they may also be found at the
craniocervical junction. In addition, cysts may occur posterior to th
e chord. Microsurgical removal is usually effective in the treatment o
f these cysts.