We report on a 25 year old woman with aplasia of the Mullerian duct, u
nilateral renal agenesis, and anomalies of the cervicothoracic somites
(MURCS association). Growth retardation and facial asymmetry were als
o present. A review of published reports allows MURCS association to b
e distinguished from related associations, sequences, and syndromes. M
oreover, sporadic occurrence, the broad spectrum of associated anomali
es, and the involvement of different organ systems closely related in
early embryogenesis are arguments for considering MURCS association as
the consequence of a developmental field defect.