21 YEARS ON PERIODIC HEMODIALYSIS IN A PA TIENT WITH PRIMARY HYPEROXALURIA

We report a male patient with primary hyperoxaluria from childhood who survived more than 21 years on conventional haemodialysis. Despite th e severity of his bone disease, he was married and actively employed u p until 2 years before his death. His condition really worsened a few months before his death. He presented with only renal and bone involve ment and had hardly any cardiovascular complications, that was probabl y a reason for his prolonged survival. Such an evolution is very unusu al and we speculate that the length of haemodialysis sessions in addit ion to the large surface of the membrane probably contributed to such an outcome. During the time period on HD, anemia was transiently contr olled by recombinant erythropoietin despite oxalate involvement of the marrow. He was refused a liver-kidney transplant and died from malnou rishment at 43 years of age. To our knowledge, such an outcome has not yet been reported. It shows that careful prolonged hemodialysis sessi ons should be helped in admet patients without severe cardiovascular i nvolvement.