STATUS OF SURVIVORS AFTER ATRIAL REDIRECTION FOR TRANSPOSITION OF THEGREAT-ARTERIES - A COMPLETE LONG-TERM FOLLOW-UP

All 32 survivors with transposition of the great arteries, born in 196 4-83 and operated on at our institution using atrial redirection, were evaluated by cardiac catheterization, echocardiography and Holter mon itoring, There were 17 Mustard patients, age 17.1 years (+/-3.5, 12.0- 22.0) and 15 Senning patients, age 9.4 years (+/-1.6, 7.2-12.1). All b ut one had simple transposition. Six had caval obstruction, one had pu lmonary venous obstruction, three had large atrial shunts, four had co nsiderable pulmonary hypertension, seven had mild ventricular outflow tract obstruction, four had significant tricuspid regurgitation, II ha d systemic ventricle dysfunction (one severe), 14 had sinus node dysfu nction (three symptomatic) and two had atrioventricular block (one wit h pacemaker). Eight Mustard patients (47%) and one Senning patient (7% ) had symptomatic cardiac sequelae, and only one patient (Senning) was free from sequelae, illustrating that these patient groups will need continuing medical attention.