PSEUDOMYXOMA PERITONEI ORIGINATING FROM A TERATOMA OF THE OMENTUM WITH A PREDOMINANT MUCINOUS BORDERLINE COMPONENT

A mature cystic teratoma of the omentum occurred in a 37 years old wom an, who had an appendicectomy at the age of 8. This extragonadal terat oma contained a predominant mucinous glandular pattern of borderline m alignancy, responsible for pseudomyxoma peritonei. Ovarian biopsies ha d only shown surface mucinous deposits at the time of the first laparo tomy but two years later ovarian mucinous cystadenomas of borderline m alignancy appeared. The patient developped intestinal obstruction, sur round by mucinous retractil material and died four years and an half a fter initial diagnosis. This case is, to our knowledge, the first pseu domyxoma peritonei occurring from an extragonadal teratoma, the events chronology suggesting the secondary nature of the ovarians tumors.