PULMONARY VALVULAR STENOSIS ASSOCIATED WITH TAKAYASUS DISEASE - FAVORABLE RESPONSE TO CORTICOSTEROIDS - A CASE-REPORT

The authors describe the first reported case of type IV Takayasu's art eritis with pulmonary valve stenosis. After thirty months under cortic osteroid therapy the disappearance of the pulmonary valve stenosis sig ns was observed in the patient. In the same patient coarctation of the aorta, aortic insufficiency, stenosis of both pulmonary arteries, and left coronary artery stenosis were observed. This case illustrates th e extensive cardiovascular involvement that can occur in Takayasu's ar teritis and suggests that pulmonary valvular stenosis could be seconda ry to the same inflammatory process.