H. Opitz et al., GIANT-CELL TUMOR OF THE OCCIPITAL BONE IN A CASE OF VON RECKLINGHAUSEN NEUROFIBROMATOSIS, Clinical neuropathology, 15(4), 1996, pp. 226-230
Von Recklinghausen neurofibromatosis (NF1) is the most common heredita
ry syndrome predisposing to neoplasia. The most common symptomatic man
ifestation of NF1 is the plexiform neurofibroma. We describe the case
of a patient with classical von Recklinghausen neurofibromatosis prese
nting with a giant cell tumor (GCT) of the occipital bone infiltrating
a surrounding plexiform neurofibroma.