RARE INHERITED COAGULATION DISORDERS IN INDIA

Twenty four cases with rare coagulation disorders were diagnosed over a 4 year period. These included 8 patients with factor X deficiency, 7 with factor XIII deficiency, 4 each with fibrinogen and factor VII de ficiency and 1 with factor V deficiency. All these patients had presen ted with bleeding manifestations. Two patients with factor X deficienc y showed interesting clinical presentations, one patient had recurrent deep vein thrombosis and another patient had a pseudotumor of the thi gh.