Primary intracranial rhabdomyosarcoma is extremely rare. Here, a case
that is most consistent with a botryoid rhabdomyosarcoma is described
in a 4.5-year-old boy. The case is unique because it was preceded by a
congenital Dandy-Walker malformation, choroid plexus hyperplasia and
an enormous oversecretion of cerebrospinal fluid during infancy.