A prospective study of seven consecutive patients with congenital arac
hnoid cysts treated endoscopically is reported. The ages of the patien
ts at the time of diagnosis ranged from 5 to 47 years with three patie
nts under 15 years. Two cysts were located in the posterior cranial fo
ssa, four in the middle cranial fossa, and one in the suprasellar-prep
ontine area. The patients' symptoms included headache, seizures, vomit
ing, nausea, dizziness, balance problems, and precocious puberty. The
authors performed cystocisternostomies and ventriculocystostomies via
burr holes with the aid of a universal neuroendoscopic system. Minor b
leeding was easily controlled by rinsing. In one case, the endoscopic
procedure had to be abandoned because of significant bleeding, which o
bscured a clear operative view, and an open microsurgical cyst fenestr
ation was performed. The follow-up review periods in this group of pat
ients ranged from 15 to 30 months. There was no mortality or morbidity
. Symptoms were relieved in five patients and improved in one. Pre coc
ious puberty in one case continued. In six cases, follow-up magnetic r
esonance images or computerized tomography scans revealed a decrease i
n the size of the cysts. Although the follow-up period is too shea to
make statements on long-term outcome, the authors recommend the minima
lly invasive endoscopic approach for treatment of arachnoid cysts as t
he first therapy of choice. Should the endoscopic procedure fail, esta
blished treatment options such as microsurgical fenestration or cystop
eritoneal shunting can subsequently be performed without causing addit
ional risk to the patient.