A 49-YEAR-OLD WOMAN WITH DYSPNEA, PALPITATIONS AND SYNCOPE

Pulmonary hypertension is rarely described in association with Sjogren 's syndrome. The authors report the case of a patient in which pulmona ry hypertension was the inaugural clinical manifestation of primary SJ ogren's syndrome. Clinical assessment, differential diagnosis, etiopat hological implications, and therapeutic approach are discussed.