PRIMARY SYSTEMIC AMYLOIDOSIS - A REPORT OF 2 CASES

Authors
DEZFOULIAN B ARRESE JE FERNANDEZ A STAS I BARTHE L HANSEN I PIERARD GE DELABRASSINNE M LAPIERE CM
Citation
B. Dezfoulian et al., PRIMARY SYSTEMIC AMYLOIDOSIS - A REPORT OF 2 CASES, Dermatology, 192(4), 1996, pp. 413-415
Citations number
15
Categorie Soggetti
Dermatology & Venereal Diseases
Journal title
Dermatology → ACNP
ISSN journal
10188665
Volume
192
Issue
4
Year of publication
1996
Pages
413 - 415
Database
ISI
SICI code
1018-8665(1996)192:4<413:PSA-AR>2.0.ZU;2-6
Abstract
We report 2 cases of primary systemic amyloidosis. A monoclonal gammop athy was confirmed at the postmortem examination of the first patient. An extensive search for evidence of chronic infection, inflammation, neoplasms and paraproteinemia was conclusively negative in the other p atient. The recognition of cutaneous signs of primary systemic amyloid osis is crucial to insure a rapid management aimed at postponing the f atal issue of the disease.