ATRESIA OF THE LEFT-SIDED ATRIOVENTRICULA R VALVE WITH SINGLE VENTRICLE AND TRANSPOSITION OF THE GREAT-ARTERIES IN AN ADULT PATIENT

Mitral atresia is an extremely rare congenital anomaly in which surviv al into adulthood is an exception. Without treatment most patients wit h this anomaly will die in early childhood and only few reach adolesce nce or early adulthood. The here described patient with mitral atresie , atrial septal defect, single ventricle and transposition of the grea t arteries survived to age 24 years. She died as consequence of massiv e cerebral embolism of a thrombus in her left atrium.