ARTERIOVENOUS MALFORMATION ASSOCIATED WITH MOYAMOYA DISEASE

The first case of a child with an arteriovenous malformation (AVM) ass ociated with moyamoya disease is reported. The patient presented ische mic symptoms and underwent indirect bypass surgery on both sides when she was 5 years old. Four years later she suffered from headache, and a small AVM of the left frontal lobe associated with the moyamoya vess els was detected. Single photon emission computed tomography (SPECT) w as performed at age ii and demonstrated low local cerebral blood flow (CBF) in the left frontal lobe and right temporal lobe, although the r evascularization after the bypass surgery seemed to be effective, as j udged on pancerebral angiography. We feel that brain ischemia due to t he moyamoya disease may have played a causative role in the developmen t of the AVM.