NONTERATOID MEDULLOEPITHELIOMA OF THE RETINA WITH ELECTRON-MICROSCOPIC AND IMMUNOHISTOCHEMICAL CHARACTERIZATION

Medulloepitheliomas are rare intraocular tumor predominant in children , and original mainly from undifferentiated nonpigmented epithelium of the ciliary body. These tumors rarely involve the optic nerve or the retina. They are classified as nonteratoid and teratoid types; the lat ter contains heterologous tissues. The teratoid variant of medulloepit heliomas involving the optic nerve or the retina is reported in four p atients only. We describe the first case of a benign nonteratoid medul loepithelioma of the retina in a 3 1/2-year-old girl with immunohistoc hemical and electron microscopic characterization.