Two patients with superficial siderosis of the central nervous system
are reported, Both developed progressive deafness over many years; one
with associated anosmia and partial seizures; the other with progress
ive ataxia and diplopia, The cerebrospinal fluid was xanthochromic In
one and the protein was raised in both, Magnetic resonance imaging rev
ealed a hypodense rim around the eighth cranial nerve, cerebellum, bra
in stem and spinal cord. Despite extensive investigations the cause of
the superficial siderosis in both patients remains undetermined.