EHLERS-DANLOS SYNDROME WITH A SPONTANEOUS CAROTICOCAVERNOUS FISTULA OCCLUDED BY DETACHABLE BALLOON - CASE-REPORT AND REVIEW OF LITERATURE

We report a caroticocavernous fistula (CCF) treated by an endovascular procedure in a young woman with Ehlers-Danlos syndrome type IV, with severe bilateral carotid and vertebral artery dysplasia. The CCF, whic h appeared after minor trauma, was successfully occluded by a detachab le balloon introduced into the venous side by an arterial approach. Si x previously published cases are reviewed, five successfully treated. The difficulties and risks of the endovascular procedure due to the va scular changes, are emphasised. The possibility of the venous approach is discussed.