Vertigo, an extremely common symptom, may be caused by numerous disord
ers affecting the central or peripheral vestibular systems. Patients c
an usually be categorized into four groups based on the clinical prese
ntation: monophasic, prolonged episodes of vertigo due to acute unilat
eral vestibular hypofunction; recurrent episodes of vertigo, due to tr
ansient vestibular dysfunction; vertigo provoked by changes in head po
sition with respect to gravity (positional vertigo); and bilateral ves
tibulopathies, which present with imbalance and oscillopsia. Although
each clinical syndrome is usually caused by a limited number of disord
ers, many less common entities must be considered in the differential
diagnosis. This article reviews the clinical presentation of the less
common causes of vestibular syndromes and discusses their medical and
nonmedical management.