Malignant schwannomas are rare. These malignomas are primary nerve she
ath tumors that usually arise from a peripheral nerve. They appear mos
t frequently in the lower extremities, including the hips and buttocks
(34.8%), the upper extremities (23.4%), and in the trunk (17%). To th
e best of our knowledge, this is the First reported case of a malignan
t schwannoma of the rectum. We describe the rare disease with referenc
e to the literature.