Endodermal sinus tumor is an uncommon malignant germ-cell neoplasm. Th
ese tumors usually present in childhood or young adulthood as testicul
ar or ovarian masses, however, mediastinal and intracranial tumors hav
e been described. The authors report the occurrence of a primary paras
pinal endodermal sinus tumor in a 21-month-old boy who presented with
thoracic spinal cord compression. A review of the literature failed to
reveal a similar case. The clinical presentation, radiographic charac
teristics, operative findings, and patient outcome are discussed.