The neurogenic tumors in the biliary tract are rare and usually are am
putation neuroma that occur after cholecystectomy. We describe a case
of isolated neurofibroma of the common bile duct in a young man not ch
olecystectomized. The patient suffered recurrent episodes of abdominal
pain, vomiting and weight loss without clinical signs of Von Reckling
hausen's disease or jaundice. The hepatogram was normal. The echograph
y indicated a solid formation with obstruction of the proximal common
bile duct. In the ERCP the stenosis was found. Surgical excision of th
e tumor and anastomosis of bilateral hepatic ducts and jejunum were ca
rried out. At microscopic examination intraparietal neurofibroma of th
e common bile duct was found. As isolated entity, we know of only one
reported case.