Pj. Vignos et al., EVALUATION OF A PROGRAM FOR LONG-TERM TREATMENT OF DUCHENNE MUSCULAR-DYSTROPHY - EXPERIENCE AT THE UNIVERSITY HOSPITALS OF CLEVELAND, Journal of bone and joint surgery. American volume, 78A(12), 1996, pp. 1844-1852
One hundred and forty-four boys who had Duchenne muscular dystrophy we
re managed at a single center between 1953 and 1994 and were followed
for a mean of 8.9 years. The long duration of follow-up provided an op
portunity to examine the effects of physical therapy and orthopaedic t
reatment on contractures of the lower extremities and on the duration
of the ability to walk. Contractures of the lower extremities were con
trolled best when patients were managed with a combination of daily pa
ssive stretching exercises, prescribed periods of standing and walking
, tenotomy of the Achilles tendon, posterior tibial-tendon transfer, a
nd application of knee-ankle-foot orthoses. Approximately two years af
ter bracing, the severity of the contracture of the heel cords was sim
ilar in the patients who had had an operation and those who had not. B
y the fourth year after bracing, however, the patients who had had an
operation had less severe contractures than those who had had bracing
alone. Five to seven years after the operation and bracing, control of
contractures was still good, especially for the patients who had had
posterior tibial-tendon transfer. Contracture of the knee was well con
trolled five to seven years after bracing in all patients who had had
bracing, with or without an operation. The program enabled the patient
s who had been managed with bracing to walk until a mean age of 13.6 y
ears. After loss of the ability to walk with bracing, the ability to s
tand continued for an additional two years with use of orthoses. The f
indings of the present study demonstrate the value of traditional meth
ods of operative treatment and bracing for controlling contractures of
the lower extremities in patients who have Duchenne muscular dystroph
y and for prolonging their ability to walk.