We report an adult female with a rare giant choledochal cyst. The pati
ent presented following a normal pregnancy with the classical triad of
an abdominal mass associated with jaundice and right upper quadrant a
bdominal pain. The cyst was excised using an intramural technique and
biliary reconstruction achieved with a Roux-en-Y hepaticojejunostomy.
Our patient has remained well with no evidence of malignancy over a 12
year review period. The aetiology and current management of this cond
ition are discussed.