UNGUARDED TRICUSPID ORIFICE - A RARE MALFORMATION OF TRICUSPID-VALVE DIAGNOSED BY ECHOCARDIOGRAPHY - REPORT OF 2 CASES AND REVIEW OF THE LITERATURE

In this report we present two cases with unguarded tricuspid orifice, and review the literature. The complete absence of tricuspid valvular structures is a very rare anomaly coexisting with pulmonary atresia an d intact ventricular septum, and is termed unguarded tricuspid orifice . Double tricuspid orifices and isolated dextrocardia were distinguish ing features of our first case, The second patient of this report, a 5 -year-old boy, is the first case in the literature with this malformat ion of the tricuspid valve as an isolated anomaly, in addition to bein g the first surviving case in the literature.