EPITHELOID SARCOMA OF THE PAROTID REGION

Background: Epitheloid sarcoma has been described in 1970 by Enzinger as a separate tumor entity. It is a rare soft-tissue tumor mostly foun d in the distal extremities in young adults. The head and neck region is only very infrequently affected. Patient and result: We report the rare case of a manifestation of an epitheloid sarcoma in the area of t he right parotid gland in a 72-year-old patient; Only two more cases w ith a similar tumor entity and location have been described in the int ernational literature. The patient underwent total parotidectomy, radi cal neck dissection, and postoperative radiotherapy two years ago and has been free of recurrence since then. Conclusions. Epitheloid sarcom as of the head and neck are very rare tumors. They are treated by radi cal local tumor removal, neck dissection, and postoperative radiothera py. Prolonged postoperative follow-up is necessary since recurrences c an occur after up to more than 15 years.