We report a case of a rare congenital nasal malformation. A young male
patient was seen with a unilateral duplication of the left nostril. A
ccording to the morphogenetic classification, described by van der Meu
len, this nasal malformation could be classified as a type IV nasal dy
splasia. The other observed abnormalities that were seen were part of
the CHARGE association, which is defined as coloboma of the iris, hear
t deformities, choanal atresia, retarded growth, genital and ear defor
mities. The patient underwent a surgical correction of the nose using
an L-approach, yielding a satisfactory result 1 year postoperatively.
Details of the case and a review of the scarce literature are presente
d.