H. Chabriat et al., HEMIPLEGIA CAUSED BY STURGE-WEBER ANGIOMA TOSIS WITHOUT CEREBRAL INFARCTION IN TERM PREGNANCY, Revue neurologique, 152(8-9), 1996, pp. 536-541
During the third quarter of her pregnancy, a young woman with Sturge-W
eber angiomatosis hud a severe right hemiplegia with hemianopia and ap
hasia, followed 48 hours later by focal seizures. Neuroimaging did not
show any cerebral lesion but contrast magnetic resonance imaging reve
aled a left hemispheric pial angiomatosis. The patient recovered progr
essively from the third day after a ceasarean. The hemianopia disappea
red within 15 days. the hemiplegia within one month and the aphasia gr
eatly improved within 3 months. Ten weeks after the clinical onset, we
performed a positron emission tomography study. A decrease from 15 to
40% of the cerebral radioactivity was observed after injection of wat
er ((H2O)-O-15) or fluorodesoxyglucose ((18)FDG) in the left temporooc
cipital area adjacent to the meningeal angiomatosis. A chronic and foc
al olighemia, already reported in Sturge-Weber angiomatosis, might par
ticipate in the occurrence of this cortical metabolic depression.