AN ATYPICAL CASE OF MONONEURITIS MULTIPLEX IN PRIMARY SJOGRENS-SYNDROME

We present an atypical case of peripheral nervous system (PNS) involve ment in Sjogren's syndrome in a 63 year-old woman. Symptoms of an entr apment neuropathy were the first manifestation of the systemic disease and they mere subsequently coupled to those of a mononeuritis multipl ex. Clinical and laboratory signs for the diagnosis of Sjogren's syndr ome became subsequently overt. The mononeuritis multiplex remained cli nically limited to the upper limbs and characterized by unusually seve re motor symptoms which progressed up to the development of a final co mplete deplegia. By contrast, sensory symptoms at the upper limbs rema ined mild over the entire course of the disease and the lower limbs re vealed a subclinical sensory-motor damage only during the late stage.