Leiomyosarcoma of the larynx is extremely rare, only 21 cases were rep
orted in the literature. The authors report a personal case in a 26 Se
ars old patient treated by a total laryngectomy and analyse all cases
of the literature. Il comes in relative yooung man (42 years old) in r
egard to the others ORL localisations. There is not tobacco relation.
The lymph node extension is rare however the distant metastasis are fr
equent specially in lung. The treatment is based on surgery, the neck
lymphadenectomy is posible in patients with cervical lymph nodes. The
Leiomyosarcoma is a resistant tumor to the irradiation and chemotherap
y however the postoperative irradiation is justified. The prognosis of
this tumor is reserved on account of local recurences and distant met
astasis.