Cochlear implantation is now a routine clinical procedure for deaf pat
ients in many countries (Gibson, 1987). It replaces the function of da
maged cochlear hair cells and, therefore, detects sound and by electri
cal stimulation produces an appropriate signal in the remaining cochle
ar nerve fibres (House and Berliner, 1991). Wegener's granulomatosis i
s an uncommon auto-immune disease. It has a peak incidence at the fift
h decade with slight male predominance. Nasal problems are the predomi
nant presentation with otological manifestations presenting rarely. We
report a case of Wegener's granulomatosis presenting with total heari
ng loss and after right cochlear implantation a free held threshold of
40 dB and 20 per cent Bamford-Kowal-Bench (BKB) speech test. We concl
ude that Wegener's granulomatosis is not an absolute contraindication
for cochlear implantation.