TETRALOGY OF FALLOT WITH ABSENT PULMONARY VALVE - PRENATAL-DIAGNOSIS AND MANAGEMENT IN THE 2ND TRIMESTER

Tetralogy of Fallot with absent pulmonary valve is a rare congenital c ardiac malformation detected in 3% to 6% of tetralogy of Fallot patien ts. The prognosis depends on respiratory complications. In the present case the diagnosis was made at 18 week's gestation with two-dimension al and Doppler echocardiography. A ventricular septal defect and overr iding aorta, absent valve echo, pulmonary regurgitation, and cystic pu lsatile dilatation of the left pulmonary artery were the main diagnost ic criteria. Severe respiratory complications were assumed in combinat ion with a hyperechogenic left lung and termination of pregnancy was p erformed at 20 weeks' of gestation.