CONGENITAL MICROGASTRIA, GROWTH-HORMONE DEFICIENCY AND DIABETES-INSIPIDUS

Microgastria is a rare malformation of the stomach always associated w ith variable patterns of malformations of the lung, heart, aortic arch , skeleton, and central nervous system. Many cases present with asplen ia and hepatic symmetry as well as intestinal malrotation. We report a first case of a 4.5-year-old girl with congenital microgastria in ass ociation with growth hormone deficiency, diabetes insipidus, brachyoes ophagus, hernia of the diaphragm, gastro-oesophageal reflux, intestina l malrotation, enlarged symmetrical liver, asplenia, as well as mental and statomotor retardation. Conclusion Congenital microgastria is alw ays associated with malformations of other organs, Patients at any age presenting one of the symptoms: failure to thrive, vomiting, asplenia , midline defects and parts of the VACTERL association should be caref ully examined to exclude microgastria.