Apical hypertrophic cardiomyopathy was defined initially by three elec
trocardiographic and angiographic criteria : the presence of giant (ov
er 10 mm) inverted T waves in leads V4 and VS of the resting ECG; an '
'ace of spades'' appearance of left ventricular angiography in end dia
stole in the right anterior oblique projection the electrocardiographi
c sum RVS + SV1 greater than 35 mm. There after, authentic cases of ap
ical hypertrophy have been demonstrated by imaging techniques or obser
ved anatomically without the presence of these three criteria. The aut
hors review the epidemiological, clinical and paraclinical features of
this particular form of hypertrophic cardiomyopathy.