We report a patient with naevoid basal cell carcinoma syndrome (NBCCS)
who developed cutaneous cysts on her digits, Histological examination
of one of the cysts showed a festooned lining epithelium maturing wit
hout a granular cell layer, similar to that of the jaw keratocyst char
acteristic of this syndrome, This type of cutaneous keratocyst has bee
n reported only once previously, in two patients with NBCCS.