An unusual case of congenital hydrocephalus and visual Loss due to dev
elopmental tumour of optic pathways is described. Diffuse. uniform and
symmetrical replacement and enlargement of optic nerves, chiasma and
optic tracts resulted in remarkable computerized tomographic (CT) scan
images not yet described in the literature. Embryo-pathogenesis of th
is anatomical configuration of the neoplasm outlining the enlarged vis
ual pathways in their entirety is discussed. The relevant literature i
s reviewed.