Malignant retroperitoneal schwannoma is an extremely rare tumor, with
only six cases previously reported occurring in the perirenal space. W
e herein report the seventh case. A 50-year-old woman presented with a
n abdominal. mass suggestive of renal cell carcinoma by standard preop
erative evaluation. The tumor required surgical exploration and pathol
ogic evaluation for diagnosis. The final histologic diagnosis was made
with the aid of electron microscopy and immunohistochemical staining
with antibodies for S-100 protein.