4TH VENTRICULAR HEMANGIOBLASTOMA ASSOCIATED WITH PHEOCHROMOCYTOMA ANDRENAL MEDULLARY FIBROMA

Intraventricular hemangioblastomas are exceptionally rare. Of the case s described in the literature, very few were associated with von Hippe l-Lindau disease. We present a highly unusual case of a fourth ventric ular hemangioblastoma associated with a pheochromocytoma and a renal m edullary fibroma. This may represent a forme fruste of the von Hippel- Lindau complex. A workup for papilledema resulted in the discovery of this rare finding.