HEMANGIOBLASTOMA OF THE RADIAL NERVE - CASE-REPORT

A CASE OF hemangioblastoma of the right radial nerve is presented. Hem angioblastomas are rare vascular neoplasms characteristically associat ed with the Von Hippel-Lindau syndrome, in which they are found in the retina, the posterior fossa, and, less often, the spinal cord. Though t of as primary central nervous system neoplasms, hemangioblastomas ar e rarely found adjacent to the spinal cord involving proximal nerve ro ots, which represent border zones between the central and peripheral n ervous systems. We could find no other report of a pure hemangioblasto ma situated this far distally in the peripheral nervous system. The hi stological findings, immunohistochemistry, and electron microscopic fi ndings of this lesion are discussed. This case supports the hypothesis that hemangioblastoma is not derived from astrocytes, because of the location of this tumor in the peripheral nervous system and glial fibr illary acidic protein negativity.