Tumoral calcinosis is a rare systemic disorder characterized by para-a
rticular ectopic soft-tissue calcification. This case report describes
the ophthalmic features (palpebral conjunctival calcific nodules, the
white limbal girdle of Vogt, disc drusen, and angioid streaks) in a 3
8-year-old Asian woman who had tumoral calcinosis associated with hype
rphosphatemia. A morphologic study of the calcified nodules on the pal
pebral conjunctiva disclosed deposition of hydroxyapatite crystals in
an extracellular matrix (deposit) containing alcianophilic mucopolysac
charides. Excision of the eyelid nodules was not followed by recurrenc
e.