We describe a patient with livedo racemosa generalisata (LRG), Raynaud
's phenomenon, multifocal recurring transitory and complete ischemic a
ttacks and laboratory findings of systemic inflammation. Working diagn
oses were vasculitis, mixed connective tissue disease, or Sneddon's sy
ndrome, but echocardiography revealed a left atrial myxoma. Special st
aining of skin biopsies with alcian-blue showed arterial occlusion cau
sed by myxomatous material. Arterial embolism by parts of the myxoma i
s suggested to be the cause of the LRG and probably the neurological f
indings.