SEGMENTAL MULTICYSTIC KIDNEY AND IPSILATERAL DUPLICATION ANOMALIES

Purpose: We characterize segmental multicystic dysplasia, in which the re is a duplex collecting system with multicystic changes in the upper pole. Materials and Methods: Three neonates with an abdominal mass an d/or prenatal diagnosis of a multicystic kidney were evaluated. Postna tal ultrasound showed a classic multicystic kidney and small ipsilater al orthotopic ureterocele in all cases. All patients had ipsilateral g rade V lower pole reflux and a renal scan showed functioning lower pol e systems. Results: One patient underwent bilateral ureteroneocystosto my and another underwent upper pole nephrectomy. There has been reduct ion in the size of the segmental multicystic kidney in 2 patients and decrease in reflux grade in 2 (followup 2 to 5 years). Conclusions: Ne wborns with an apparent multicystic kidney should undergo a voiding cy stourethrogram and renal scan to confirm the diagnosis. Segmental mult icystic kidney can be followed nonoperatively in most cases because th e cysts tend to involute.