A series of 128 acoustic neuromas (ANs) managed in our center in the l
ast 6 years were evaluated. Sixteen cases (12.5%) were found to have n
ormal pure tone audio-grams comparatively younger age was an important
characteristic of these patients. Tinnitus, dysequilibrium, and subje
ctive hearing loss or distortion were their most common complaints. Pu
re tone audiometry showed a mean pure tone average of 14.5 dB. Speech
discrimination score and performance intensity phonetically balanced i
ndex were very insensitive and showed very high false-negative results
. Auditory brainstem responses proved to be a reliable test, being pos
itive in 93.8% of cases. The mean tumor size did not show any signific
ant difference when compared with acoustic neuroma cases with abnormal
hearing. The combination of otologic and neurotologic symptoms in a y
oung patient should prompt the clinician to investigation further even
if hearing is within normal limits. A high index of suspicion is a pr
erequisite for the early diagnosis of such subtle lesions.