Hair follicle nevus has been variously defined as a specific type of n
eoplasm with follicular differentiation or as a synonym for trichofoll
iculoma; the latter view has predominated in recent years. We report a
nodular lesion that was identified histopathologically as a hamartoma
with follicular differentiation and that systematic serial sectioning
showed not to be a trichofolliculoma. After reviewing previous descri
ptions of lesions diagnosed as hair follicle nevus, and in the light o
f our own observations, we believe that hair follicle nevus is a disti
nct type of adnexal hamartoma.