ANESTHESIA FOR RETT-SYNDROME

Authors
DEARLOVE OR WALKER RWM
Citation
Or. Dearlove et Rwm. Walker, ANESTHESIA FOR RETT-SYNDROME, Paediatric anaesthesia, 6(2), 1996, pp. 155-158
Citations number
9
Categorie Soggetti
Anesthesiology,Pediatrics
Journal title
Paediatric anaesthesia → ACNP
ISSN journal
11555645
Volume
6
Issue
2
Year of publication
1996
Pages
155 - 158
Database
ISI
SICI code
1155-5645(1996)6:2<155:AFR>2.0.ZU;2-S
Abstract
Rett syndrome is a devastingly disabling neurological disease that is only observed in girls. Scoliosis occurs in roughly half the girls and surgery may be required. Anaesthesia is described in three patients. Sudden death may be a feature of the disease which occurred four weeks postoperatively in one case. Although a long QT, interval may be seen , it did not occur in any of our cases.