EPILEPSY IN THE NEVOID BASAL-CELL CARCINOMA SYNDROME (GORLIN SYNDROME) - REPORT OF A CASE DUE TO A FOCAL NEURONAL HETEROTOPIA

Authors
HOGAN RE TRESS B GONZALES MF KING JO COOK MJ
Citation
Re. Hogan et al., EPILEPSY IN THE NEVOID BASAL-CELL CARCINOMA SYNDROME (GORLIN SYNDROME) - REPORT OF A CASE DUE TO A FOCAL NEURONAL HETEROTOPIA, Neurology, 46(2), 1996, pp. 574-576
Citations number
10
Categorie Soggetti
Clinical Neurology
Journal title
Neurology → ACNP
ISSN journal
00283878
Volume
46
Issue
2
Year of publication
1996
Pages
574 - 576
Database
ISI
SICI code
0028-3878(1996)46:2<574:EITNBC>2.0.ZU;2-8
Abstract
We present a case of uncontrolled temporal lobe epilepsy due to a foca l left temporal neuronal heterotopia associated with the nevoid-basal- cell carcinoma syndrome. This is the first pathologically described le sion associated with temporal lobe epilepsy in this syndrome. Because the patient's seizures resolved after a modified left anterior tempora l lobectomy, this case illustrates that epilepsy in patients with the nevoid basal-cell carcinoma syndrome is potentially curable and should be investigated appropriately.