A 47-year-old man was admitted for evaluation of unsteady gait, postur
al instability, and dysarthria. On admission, neurological examination
s revealed cerebellar ataxia, extrapyramidal signs including parkinson
ism and positive Trousseau's sign, Laboratory findings revealed severe
hypocalcemia and hyperphosphatemia, and serum intact parathyroid horm
one was not detectable, Brain computed tomography revealed severe calc
ification of basal ganglia and dentate nuclei, He was diagnosed as idi
opathic hypoparathyroidism; treatment with 1 alpha (OH) vitamin D-3 br
ought marked improvement of neurological manifestations. We report a r
are case of idiopathic hypoparathyroidism presenting with extrapyramid
al and cerebellar dysfunction with a review of literature.