S. Nawa et al., CLINICAL AND ANGIOGRAPHIC ANALYSIS OF CONGENITAL CORONARY-ARTERY FISTULAS IN ADULTHOOD - IS THERE ANY NEW TREND, Japanese Heart Journal, 37(1), 1996, pp. 95-104
Fifteen (2.1%) patients were diagnosed as having congenital coronary a
rtery fistula (CAF) in a consecutive series of 704 adult patients unde
rgoing selective coronary arteriography; the incidence was astonishing
ly higher than previous observations. The presentation of clinical sym
ptoms and the electrocardiographic changes at rest and/or after exerci
se testing probably attributable to the CAF were observed unexpectedly
often in spite of the fact that the magnitude of the shunt seemed not
to be significant. With respect to the anatomy of the CAF, the incide
nce of origination from plural coronary arteries and that of fistulati
on into the left ventricle were also unexpectedly high. These observat
ions presented a striking contrast to those of previous reports, but w
e were unable to determine the reason. In four cases, the CAF was liga
ted either electively or concurrently with mitral valve surgery, and t
he results were satisfactory. Taking these circumstances into consider
ation, we should not minimize the impact of a CAF with a seemingly sma
ll shunt.