Malignant fibrous histiocytoma is a pleomorphic soft tissue sarcoma, w
hich constitutes only 2% of all cardiac malignancies and is typically
located in the left atrium. We report a young male patient with malign
ant fibrous histiocytoma located on, the right side of the heart. Earl
y recurrence was observed after extensive surgical resection to reliev
e symptoms of outflow tract obstruction. Noninvasive evaluation, and m
anagement with regard to the literature are discussed.